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From SNPedia

Trimethylaminuria (TMAU), also known as fish odor syndrome, is a rare metabolic disorder resulting from too little of the enzyme known as flavin containing monooxygenase 3 (FMO3). When this enzyme is not working correctly or if not enough enzyme is produced, the body loses the ability to properly convert trimethylamine (TMA) from tyramine-containing foods (such as cheese) into trimethylamine oxide (TMAO). Trimethylamine then builds up and is released in the person's sweat, urine, and breath, giving off a strong fishy odor or strong body odor.Wikipedia

Note that cases of trimethylaminuria have been reported from carriers of a single defective FMO3 allele, as well as from homozygous minor allele genotypes.