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From SNPedia

The mucopolysaccharidoses (MPS) are a group of inherited lysosomal storage disorders, in which the body is unable to properly breakdown mucopolysaccharides (long chains of sugar molecules that are found throughout the body). In individuals with MPS disorders, abnormal accumulation of certain complex carbohydrates causes progressive damage to cells, tissues, and various organ systems of the body. Inherited as autosomal recessive traits (with one exception; type II is X-linked), the different MPS subtypes and their associated genes include those in the following table.

MPS Type Name(s) Gene MOI
1 H/S Hurler/Scheie syndrome IDUA recessive
I H Hurler disease IDUA recessive
II Hunter syndrome IDS X-linked recessive
III A Sanfillipo syndrome A SGSH recessive
III B Sanfillipo syndrome B NAGLU recessive
III C Sanfillipo syndrome C HGSNAT recessive
III D Sanfillipo syndrome GNS recessive
I S Scheie syndrome IDUA recessive
IV A Morquio syndrome A GALNS recessive
IV B Morquio syndrome B GLB1 recessive
IX hyaluronidase deficiency HYAL1 recessive
VII Sly syndrome GUSB recessive
VI Maroteaux-Lamy syndrome ARSB recessive